| PubMed: | High hexacosanoic acid levels are associated with coronary artery disease. |
| PubMed: | High hexacosanoic acid levels are associated with coronary artery disease. |
| PubMed: | Reductions in neuronal peroxisomes in multiple sclerosis grey matter. |
| PubMed: | New flavan and alkyl alpha,beta-lactones from the stem bark of Horsfieldia superba. |
| PubMed: | An electrospray ionisation-mass spectrometry screening of triacylglycerols in developing cultivated and wild peanut kernels (Arachis hypogaea L.). |
| PubMed: | Zellweger syndrome - a lethal peroxisome biogenesis disorder. |
| PubMed: | Chemical composition of the fatty oils of the seeds of Cleome viscosa accessions. |
| PubMed: | Arabidopsis ECERIFERUM9 involvement in cuticle formation and maintenance of plant water status. |
| PubMed: | The effect of bone marrow transplantation on oxidative stress in X-linked adrenoleukodystrophy. |
| PubMed: | The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy). |
| PubMed: | Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation. |
| PubMed: | Inhibition of saturated very-long-chain fatty acid biosynthesis by mefluidide and perfluidone, selective inhibitors of 3-ketoacyl-CoA synthases. |
| PubMed: | A mixture of oleic, erucic and conjugated linoleic acids modulates cerebrospinal fluid inflammatory markers and improve somatosensorial evoked potential in X-linked adrenoleukodystrophy female carriers. |
| PubMed: | Is subclinical adrenal failure in adrenoleukodystrophy/adrenomyeloneuropathy reversible? |
| PubMed: | Active components from Siberian ginseng (Eleutherococcus senticosus) for protection of amyloid β(25-35)-induced neuritic atrophy in cultured rat cortical neurons. |
| PubMed: | Screening assay of very long chain fatty acids in human plasma with multiwalled carbon nanotube-based surface-assisted laser desorption/ionization mass spectrometry. |
| PubMed: | [Chemical constituents of rhizomes of Zingiber officinale]. |
| PubMed: | Phytochemical investigation of the fruit peels of Citrus reticulata Blanco. |
| PubMed: | Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy. |
| PubMed: | Lovastatin in X-linked adrenoleukodystrophy. |
| PubMed: | Investigation of stratum corneum lipid model membranes with free fatty acid composition by neutron diffraction. |
| PubMed: | Very long chain fatty acid levels in patients diagnosed with multiple sclerosis. |
| PubMed: | Fast diffusion of very long chain saturated fatty acids across a bilayer membrane and their rapid extraction by cyclodextrins: implications for adrenoleukodystrophy. |
| PubMed: | A fast method for the identification of Mycobacterium tuberculosis in sputum and cultures based on thermally assisted hydrolysis and methylation followed by gas chromatography-mass spectrometry. |
| PubMed: | [Studies on chemical constituents of aerial roots of Ficus microcarpa]. |
| PubMed: | Odd-numbered very-long-chain fatty acids from the microbial, animal and plant kingdoms. |
| PubMed: | X-linked adrenoleukodystrophy: clinical course and minimal incidence in South Brazil. |
| PubMed: | Epicuticular lipids induce aggregation in Chagas disease vectors. |
| PubMed: | Concentrations of very long-chain fatty acid in whole blood are associated with cardiovascular risk factors in children. |
| PubMed: | Plasmalogens participate in very-long-chain fatty acid-induced pathology. |
| PubMed: | A key role for the peroxisomal ABCD2 transporter in fatty acid homeostasis. |
| PubMed: | Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy. |
| PubMed: | A simple and sensitive liquid chromatographic method for the analysis of free docosanoic, tetracosanoic and hexacosanoic acids in human plasma as fluorescent derivatives. |
| PubMed: | High levels of saturated very long-chain fatty acid (hexacosanoic acid; C26:0) in whole blood are associated with metabolic syndrome in Japanese men. |
| PubMed: | Fatty acid interdigitation in stratum corneum model membranes: a neutron diffraction study. |
| PubMed: | RNAi-mediated silencing of ABCD3 gene expression in rat C6 glial cells: a model system to study PMP70 function. |
| PubMed: | [Studies on chemical constituents of Heterosmilax yunnanensis]. |
| PubMed: | Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo's oil effect. |
| PubMed: | New flavonoids and other constituents from Lespedeza cuneata. |
| PubMed: | Down-regulation of fatty acid synthase increases the resistance of Saccharomyces cerevisiae cells to H2O2. |
| PubMed: | Induction of lipid peroxidation and decrease of antioxidant defenses in symptomatic and asymptomatic patients with X-linked adrenoleukodystrophy. |
| PubMed: | Characterization of glycoinositolphosphoryl ceramide structure mutant strains of Cryptococcus neoformans. |
| PubMed: | Novel free ceramides as components of the soldier defense gland of the Formosan subterranean termite (Coptotermes formosanus). |
| PubMed: | Compounds with DNA cleaving activity from Kadsura ananosma. |
| PubMed: | Combined liquid chromatography-tandem mass spectrometry as an analytical method for high throughput screening for X-linked adrenoleukodystrophy and other peroxisomal disorders: preliminary findings. |
| PubMed: | The effect of Lorenzo's oil on oxidative stress in X-linked adrenoleukodystrophy. |
| PubMed: | Follow-up of 89 asymptomatic patients with adrenoleukodystrophy treated with Lorenzo's oil. |
| PubMed: | A novel coaxial electrospray ionization method for characterizing hexacosanoylceramides by Fourier transform ion cyclotron resonance mass spectrometry. |
| PubMed: | [Studies on the constituents from the stems of Spatholobus suberectus]. |
| PubMed: | Very long chain fatty acids activate NADPH oxidase in human dermal fibroblasts. |
| PubMed: | Constituents of Carapa guianensis Aubl. (Meliaceae). |
| PubMed: | [Studies on the chemical constituents of Chinese herb Melastoma dodecandrum]. |
| PubMed: | An HPLC-MS approach for analysis of very long chain fatty acids and other apolar compounds on octadecyl-silica phase using partly miscible solvents. |
| PubMed: | Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy. |
| PubMed: | Free radical release in C6 glial cells enriched in hexacosanoic acid: implication for X-linked adrenoleukodystrophy pathogenesis. |
| PubMed: | Antimicrobial activity of terpenoids from Trichodesma amplexicaule Roth. |
| PubMed: | [Lipid compounds from Echinacea purpurea]. |
| PubMed: | [Studies on the chemical constituents of Zanthoxylum dimorphophyllum Hemsl. var spinifolium Rhed. et Wils]. |
| PubMed: | [Studies on the chemical constituent of Ephedra likiangensis]. |
| PubMed: | [Clinical heterogeneity of X-linked adrenoleukodystrophy ]. |
| PubMed: | Diagnostic patterns of very-long-chain fatty acids in plasma of patients with X-linked adrenoleukodystrophy. |
| PubMed: | Correlations of elevated levels of hexacosanoate in erythrocyte membranes with risk factors for atherosclerosis. |
| PubMed: | Testosterone metabolites in patients reduce the levels of very long chain fatty acids accumulated in X-adrenoleukodystrophic fibroblasts. |
| PubMed: | Lovastatin therapy for X-linked adrenoleukodystrophy: clinical and biochemical observations on 12 patients. |
| PubMed: | Inactivation of the inhA-encoded fatty acid synthase II (FASII) enoyl-acyl carrier protein reductase induces accumulation of the FASI end products and cell lysis of Mycobacterium smegmatis. |
| PubMed: | Role of a new mammalian gene family in the biosynthesis of very long chain fatty acids and sphingolipids. |
| PubMed: | Progression of abnormalities in adrenomyeloneuropathy and neurologically asymptomatic X-linked adrenoleukodystrophy despite treatment with "Lorenzo's oil". |
| PubMed: | Very long-chain fatty acids in Rett syndrome. |
| PubMed: | Determination of very-long-chain fatty acids in serum by gas chromatography-nitrogen-phosphorus detection following cyanomethylation. |
| PubMed: | Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls. |
| PubMed: | A new HPLC-based method for the quantitative analysis of inner stratum corneum lipids with special reference to the free fatty acid fraction. |
| PubMed: | Inhibition of a Mycobacterium tuberculosis beta-ketoacyl ACP synthase by isoniazid. |
| PubMed: | Abnormality of very long-chain fatty acids of erythrocyte membrane in alcoholic patients. |
| PubMed: | Use of gas chromatographic fatty acid and mycolic acid cleavage product determination to differentiate among Mycobacterium genavense, Mycobacterium fortuitum, Mycobacterium simiae, and Mycobacterium tuberculosis. |
| PubMed: | Increased very long-chain fatty acids in erythrocyte membranes of patients with aceruloplasminemia. |
| PubMed: | A new peroxisomal beta-oxidation disorder in twin neonates: defective oxidation of both cerotic and pristanic acids. |
| PubMed: | Effects of exogenous hexacosanoic acid on biochemical myelin composition in weaning and post-weaning rats. |
| PubMed: | Very long-chain fatty acid pattern in crush syndrome patients in the Kobe earthquake. |
| PubMed: | Plasma phospholipid fatty acids in X-linked adrenoleukodystrophy. |
| PubMed: | Interactions of a very long chain fatty acid with model membranes and serum albumin. Implications for the pathogenesis of adrenoleukodystrophy. |
| PubMed: | Mycobacterium branderi sp. nov., a new potential human pathogen. |
| PubMed: | Measurement of peroxisomal fatty acid beta-oxidation in cultured human skin fibroblasts. |
| PubMed: | Dietary management of X-linked adrenoleukodystrophy. |
| PubMed: | Beta-oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation. |
| PubMed: | Profiles of very-long-chain fatty acids in plasma, fibroblasts, and blood cells in Zellweger syndrome, X-linked adrenoleukodystrophy, and rhizomelic chondrodysplasia punctata. |
| PubMed: | Studies on the effect of fenoprofen on the activation and oxidation of long chain and very long chain fatty acids in hepatocytes and subcellular fractions from rat liver. |
| PubMed: | Mycobacterium celatum sp. nov. |
| PubMed: | Isolation and characterization of eceriferum (cer) mutants induced by T-DNA insertions in Arabidopsis thaliana. |
| PubMed: | Altered adrenocortical response under the influence of experimentally increased serum very long chain fatty acids in rats. |
| PubMed: | Fatty acid synthesis from [2-14C]acetate in normal and peroxisome-deficient (Zellweger) fibroblasts. |
| PubMed: | Diagnosis of peroxisomal disorders with neurological involvement. |
| PubMed: | Characterization of a distinct group of slowly growing mycobacteria by biochemical tests and lipid analyses. |
| PubMed: | Schizophrenic patients treated with high dose phenothiazine or thioxanthene become deficient in polyunsaturated fatty acids in their thrombocytes. |
| PubMed: | Phospholipids in X-linked adrenoleukodystrophy white matter: fatty acid abnormalities before the onset of demyelination. |
| PubMed: | Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidation. |
| PubMed: | Oxidation of very-long-chain fatty acids in rat brain: cerotic acid is beta-oxidized exclusively in rat brain peroxisomes. |
| PubMed: | Conclusive evidence that very-long-chain fatty acids are oxidized exclusively in peroxisomes in human skin fibroblasts. |
| PubMed: | Long-chain-acyl-CoA synthetase and very-long-chain-acyl-CoA synthetase activities in peroxisomes and microsomes from rat liver. An enzymological study. |
| PubMed: | [Chemical constituents of the pericarp of Trichosanthes rosthornii Harms]. |
| PubMed: | Determination of very-long-chain fatty acids in plasma by a simplified gas chromatographic-mass spectrometric procedure. |
| PubMed: | Central nervous system malformations and white matter changes in pseudo-neonatal adrenoleukodystrophy. |
| PubMed: | Infantile phytanic acid storage disease, a disorder of peroxisome biogenesis: a case report. |
| PubMed: | Adrenomyeloneuropathy presenting as Addison's disease in childhood. |
| PubMed: | Dietary erucic acid therapy for X-linked adrenoleukodystrophy. |
| PubMed: | Gas chromatography of mycobacterial fatty acids and alcohols: diagnostic applications. |
| PubMed: | Capillary gas chromatographic analysis of mycolic acid cleavage products, cellular fatty acids, and alcohols of Mycobacterium xenopi. |
| PubMed: | Phytanic acid, pristanic acid, and very-long-chain fatty acid methyl esters measured simultaneously by capillary gas chromatography. |
| PubMed: | Very long-chain fatty acids in erythrocyte membrane phospholipids in adrenoleukodystrophy. |
| PubMed: | Hexacosanoate contents in Japanese common foods. |
| PubMed: | [Two adult cases of adrenoleukodystrophy with clinical features of striatonigral degeneration--a probable variant of adrenoleukodystrophy]. |
| PubMed: | Impaired ability of peroxisomes to activate very-long-chain fatty acids in X-linked adrenoleukodystrophy. |
| PubMed: | Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids. |
| PubMed: | Carrier detection for adrenoleukodystrophy by high-performance liquid chromatography. |
| PubMed: | Influence of structural modifications on the phase behavior of semi-synthetic cerebroside sulfate. |
| PubMed: | Treatment of infantile phytanic acid storage disease: clinical, biochemical and ultrastructural findings in two children treated for 2 years. |
| PubMed: | Effects of long-chain, saturated fatty acids on membrane microviscosity and adrenocorticotropin responsiveness of human adrenocortical cells in vitro. |
| PubMed: | Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders. |
| PubMed: | Very long chain fatty acid beta-oxidation by rat liver mitochondria and peroxisomes. |
| PubMed: | Prenatal diagnosis of Zellweger syndrome by measurement of very long chain fatty acid (C26:0) beta-oxidation in cultured chorionic villous fibroblasts: implications for early diagnosis of other peroxisomal disorders. |
| PubMed: | Electronmicroscopic study on biopsied rectal mucosa in adrenoleukodystrophy. |
| PubMed: | Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts. |
| PubMed: | Adrenoleukodystrophy: from bedside to molecular biology. |
| PubMed: | Adrenoleukodystrophy: dietary oleic acid lowers hexacosanoate levels. |
| PubMed: | A new dietary therapy for adrenoleukodystrophy: biochemical and preliminary clinical results in 36 patients. |
| PubMed: | Adrenoleukodystrophy: biochemical procedures in diagnosis, prevention and treatment. |
| PubMed: | A simple method to diagnose adrenoleukodystrophy using a dried blood spot on filter paper. |
| PubMed: | Adrenoleukodystrophy. Report of an autopsy case with adrenoleukomyeloneuropathy. |
| PubMed: | Very long-chain fatty acids in erythrocyte membrane sphingomyelin: detection of ALD hemizygotes and heterozygotes. |
| PubMed: | Analysis of mycolic acid cleavage products and cellular fatty acids of Mycobacterium species by capillary gas chromatography. |
| PubMed: | Adrenoleukodystrophy: oleic acid lowers fibroblast saturated C22-26 fatty acids. |
| PubMed: | Metabolism of [17,18-3H2]hexacosanoic acid and [15,16-3H2]lignoceric acid in cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). |
| PubMed: | Very long-chain fatty acids in neutral lipids and glycerophospholipids of adrenoleukodystrophy-cultured skin fibroblasts. |
| PubMed: | [EMG and evoked potentials in adrenomyeloneuropathy]. |
| PubMed: | Adrenoleukodystrophy without adrenal insufficiency and its magnetic resonance imaging. |
| PubMed: | Disturbed very long chain (C24-C26) fatty acid pattern in fibroblasts of patients with Zellweger's syndrome. |
| PubMed: | First trimester prenatal diagnosis of adrenoleukodystrophy by determination of very long chain fatty acid levels and by linkage analysis to a DNA probe. |
| PubMed: | [Adult disclosure of a case of familial adrenoleukodystrophy]. |
| PubMed: | Determination of C20-C30 fatty acids by reversed-phase chromatographic techniques: an efficient method to quantitate minor fatty acids in serum of patients with adrenoleukodystrophy. |
| PubMed: | Plasma and skin fibroblast C26 fatty acids in infantile Refsum's disease. |
| PubMed: | The design of a diet restricted in saturated very long-chain fatty acids: therapeutic application in adrenoleukodystrophy. |
| PubMed: | Biochemical evidence for clinically diagnosed adrenoleucodystrophy in two brothers. |
| PubMed: | The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis. |
| PubMed: | Serum very long chain fatty acid pattern in Zellweger syndrome. |
| PubMed: | The prenatal diagnosis of adrenoleukodystrophy. Demonstration of increased hexacosanoic acid levels in cultured amniocytes and fetal adrenal gland. |
| PubMed: | Increased synthesis of hexacosanoic acid (C23:0) by cultured skin fibroblasts from patients with adrenoleukodystrophy (ALD) and adrenomyeloneuropathy (AMN). |
| PubMed: | Abnormality of long-chain fatty acids in erythrocyte membrane sphingomyelin from patients with adrenoleukodystrophy. |
| PubMed: | Specificities of human and rat brain enzymes of cholesterol ester metabolism toward very long chain fatty acids: implication for biochemical pathogenesis of adrenoleukodystrophy. |
| PubMed: | Fatty acid patterns in brain, fibroblast, leukocyte and body fluid lipids in adrenoleukodystrophy. |
| PubMed: | Adrenoleukodystrophy: evidence that abnormal very long chain fatty acids of brain cholesterol esters are of exogenous origin. |
| PubMed: | Adrenoleukodystrophy: elevated C26 fatty acid in cultured skin fibroblasts. |
| PubMed: | Constituents of Nealchornea yapurenis (Euophorbiaceae). |
| PubMed: | Metabolic studies of adrenoleukodystrophy. |